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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
Chiffres clés
Open Access
61 %
Mots clés
Myogenesis
Muscle dystrophy
Dystrophie musculaire oculopharyngée
Myoblast
Regeneration
Regenerative medicine
Bile salt hydrolases
Muscle strength
Myopathies
ARN
Autoimmune diseases
Gene therapy
Epigenetics
Muscle
Aged
Exon-skipping
Biomarker
2-D PAGE
Nuclear envelope
MUTATIONS
Myosin
Neuromuscular junction NMJ
Actin
Dystrophin
Sarcopenia
Pharyngeal muscle
Haploinsufficiency
Differentiation
Inflammation
Antisens oligonucleotides
Muscular dystrophy
AAV vectors
Intercellular communication
ALS
Adipose tissue
Muscle stem cells
GENE
Myopathy
Lamins
Transcriptomics
BINDING SPECIFICITY
Fibrosis
Agrégats de PABPN1
Dysferlinopathy
Cell therapy
Satellite cells
FAPs
Triplet expansion disease
Regulatory T cells
DNA methylation
Anti-acetylcholine receptor antibodies
APOPTOSIS
Accelerometry
Geriatric assessment
Arbovirus
Andermann syndrome
Mass spectrometry
Ageing
Myoblasts
DMD
Aggregate
RNA
Gene replacement
Pax7
Atrophy
Thérapie génique
OPMD
Oculopharyngeal muscular dystrophy
Amyotrophic Lateral Sclerosis
PABPN1 agregates
Aav-U7
Effector T cells
AChR antibodies
Functional genomics
Skeletal muscle
PABPN1
AAV
Myositis
Muscle fibrosis
Duchenne muscular dystrophy
Omics
Alphavirus
Xenograft
Cross-bridge kinetics
Metabolism
Annexin A2
Calcium
DUX4
Anti-fibrotic pharmacotherapies
Neuromuscular disease
Myotube
Autologous
Dysferlin
Antiserum
FSHD
Human
Alzheimer's disease
AUTOPHAGY
Akt
Satellite cell